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琥珀酸脫氫酶的組合因子1抗體

英文名稱(chēng) SDHAF1
中文名稱(chēng) 琥珀酸脫氫酶的組合因子1抗體
別    名 LYR motif containing 8; LYR motif-containing protein 8; LYRM8; mitochondrial; SDH assembly factor 1; SDHAF1; SDHF1_HUMAN; Succinate dehydrogenase assembly factor 1; Succinate dehydrogenase assembly factor 1 mitochondrial; Succinate dehydrogenase complex assembly factor 1.

說(shuō) 明 書(shū) 0.2ml  
研究領(lǐng)域 細(xì)胞生物  神經(jīng)生物學(xué)  
抗體來(lái)源 Rabbit
克隆類(lèi)型 Polyclonal
交叉反應(yīng) Human, 
產(chǎn)品應(yīng)用 WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500 （石蠟切片需做抗原修復(fù)） 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 21kDa
性    狀 Lyophilized or Liquid
濃    度 1mg/1ml
免 疫 原 KLH conjugated synthetic peptide derived from human SDHAF1
亞    型 IgG
純化方法 affinity purified by Protein A
儲(chǔ) 存 液 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
保存條件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.

PubMed PubMed
產(chǎn)品介紹 background:
The succinate dehydrogenase (SDH) complex (or complex II) of the mitochondrial respiratory chain is composed of 4 individual subunits. The protein encoded by this gene resides in the mitochondria, and is essential for SDH assembly, but does not physically associate with the complex in vivo. Mutations in this gene are associated with SDH-defective infantile leukoencephalopathy (mitochondrial complex II deficiency).[provided by RefSeq, Mar 2010]

Function:
Plays an essential role in succinate dehydrogenase complex (SDH) assembly, a complex involved in complex II of the mitochondrial electron transport chain. Probably acts by participating in mitochondrial biosynthesis of iron-sulfur centers for complex II.

Subcellular Location:
Mitochondrion matrix.

Tissue Specificity:
Ubiquitously expressed.

DISEASE:
Mitochondrial complex II deficiency

Similarity:
Belongs to the complex I LYR family. SDHAF1 subfamily.

Gene ID:
644096

Database links:

Entrez Gene: 644096 Human

Entrez Gene: 68332 Mouse

Entrez Gene: 100912030 Rat

Entrez Gene: 499125 Ratxy-5064R    HADHA長(zhǎng)鏈烯脂酰輔酶A脫氫酶抗體
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xy-5066R    HDL高密度脂蛋白抗體
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xy-5071R    HSD3a羥基類(lèi)固醇脫氫酶3α抗體
xy-8174R    HLX1同源異型盒基因HLX1蛋白抗體
xy-5069R    HMGCS1三羥基*基輔酶A合成酶1
xy-3757R    HSF1熱休克因子1抗體
xy-3741R    phospho-HSF1(Ser326)磷酸化熱休克因子1抗體
xy-5117R    Hsc70熱休克蛋白71抗體
xy-5124R    hHBrk1微絲相關(guān)蛋白hHBrk1抗體
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xy-4544R    H9N1 NeuraminidaseA型流感病毒H9N1神經(jīng)氨酸酶型抗體
xy-4543R    H9N1 HemagglutininA型流感病毒H9N1血凝素型抗體
xy-2969R    HPV33 E7人類(lèi)乳頭狀瘤病毒33抗體
xy-4552R    H1N1 Matrix Protein 1A型禽流感病毒H1N1蛋白抗體
xy-6950R    Hepatitis A virus polyprotein VP1甲型肝炎病毒聚蛋白VP1抗體
xy-5109R    HCLS1造血干細(xì)胞特異性蛋白抗體
xy-12436R    HIC5轉(zhuǎn)化生長(zhǎng)因子β1誘導(dǎo)轉(zhuǎn)錄因子1抗體
xy-12195R    HOXC6同源盒蛋白C6抗體
xy-12196R    HOXC4同源盒蛋白C4抗體
xy-12197R    HOXD13同源盒蛋白D13抗體
xy-10334R    Histone H1.4組蛋白H1.4樣蛋白抗體
xy-10335R    H1FOO組蛋白H1FOO抗體
xy-12194R    HOXB6同源盒蛋白B6抗體
xy-15406R    Hamartin錯(cuò)構(gòu)素蛋白抗體
xy-13542R    phospho-H1FOO (Ser20)磷酸化組蛋白H1FOO抗體
xy-15398R    HHV11 ICP22單純皰疹病毒1型轉(zhuǎn)錄調(diào)節(jié)因子ICP22抗體
xy-15399R    H2A1J H2A組蛋白家族E蛋白抗體
xy-15400R    H2BFM H2B組蛋白家族M蛋白抗體
xy-15401R    H2BFWTH2B組蛋白家族成員W蛋白抗體(睪丸特異性)